@article{oai:nagoya.repo.nii.ac.jp:00024850,
 author = {Yoshio, Araki and Yasushi, Takagi and Yohei, Mineharu and Hatasu, Kobayashi and Susumu, Miyamoto and Toshihiko, Wakabayashi},
 issue = {8},
 journal = {Childs Nervous System},
 month = {Aug},
 note = {Background Focal cerebral arteriopathy includes unifocal or multifocal lesions that are unilateral or bilateral. Large- and/or medium-sized vessels are involved and can be visualized on angiography. Case report We report a case of cerebral infarction in a 9-yearold Japanese female who presented with a transient ischemic attack. Steno-occlusion involving the distal part of the internal carotid artery, proximal middle cerebral artery, and anterior cerebral artery was observed. Digital subtraction angiography demonstrated a beaded appearance in the cervical portion of the diseased internal carotid artery. Revascularization surgery was performed 45 days after the onset. A new infarction appeared on the other side of the anterior cerebral artery territory 7 months after the first onset. Antiplatelets and vasodilators were administered, and no progression was observed during 18 months of follow-up. Genetic analysis did not show ring finger protein 213 (RNF213)- related moyamoya disease, and pathological examination revealed no characteristics of fibromuscular dysplasia. Conclusion The radiological and genetic features coincided with focal cerebral arteriopathy, which is a distinct entity from fibromuscular dysplasia and RNF213-related moyamoya disease.},
 pages = {1405--1409},
 title = {Rapid Contralateral Progression of Focal Cerebral Arteriopathy Distinguished from RNF213-related moyamoya disease and fibromuscular dysplasia},
 volume = {33},
 year = {2017}
}