WEKO3
アイテム
{"_buckets": {"deposit": "462ee7ac-4c34-479d-9d39-5a69235e2e12"}, "_deposit": {"id": "27957", "owners": [], "pid": {"revision_id": 0, "type": "depid", "value": "27957"}, "status": "published"}, "_oai": {"id": "oai:nagoya.repo.nii.ac.jp:00027957", "sets": ["501"]}, "author_link": ["91029", "91030", "91031", "91032", "91033", "91034", "91035", "91036", "91037", "91038", "91039", "91040", "91041", "91042", "91043", "91044", "91045", "91046", "91047", "91048", "91049", "91050", "91051", "91052", "91053", "91054"], "item_10_biblio_info_6": {"attribute_name": "書誌情報", "attribute_value_mlt": [{"bibliographicIssueDates": {"bibliographicIssueDate": "2018-11", "bibliographicIssueDateType": "Issued"}, "bibliographicIssueNumber": "2", "bibliographicPageEnd": "133", "bibliographicPageStart": "127", "bibliographicVolumeNumber": "92", "bibliographic_titles": [{"bibliographic_title": "Journal of Dermatological Science", "bibliographic_titleLang": "en"}]}]}, "item_10_description_4": {"attribute_name": "抄録", "attribute_value_mlt": [{"subitem_description": "Background: Congenital ichthyoses (CIs) adversely affect quality of life (QOL) in patients. However, the effects of CIs on patient QOL have not been studied sufficiently. Objective: To investigate the association between disease severity and QOL in patients with harlequin ichthyosis (HI) and ichthyosis: syndromic forms (ISFs) Methods: Clinical information of patients with HI and ISFs from 2010 to 2015 were obtained from 100 dermatology departments/divisions of principal institutes/hospitals throughout Japan. We examined the relationship between disease severity and QOL in patients with HI and ISFs. Patients who were aged 8 years or older and participated in a multicenter retrospective questionnaire survey in Japan were assessed by dermatology life quality index (DLQI, range of 0–30) and clinical ichthyosis score (range of 0–100). Results: Netherton syndrome patients had a significantly higher risk of allergy to food or environmental allergens than patients with other phenotypes. Keratitis-ichthyosis-deafness (KID) syndrome patients showed a significantly higher risk of skin infections than patients with other phenotypes. Complete data on DLQI were obtained from 13 patients, whose median age was 21 (8–71) years. Nine patients were male, and 4 were female. Systemic retinoids were administrated to 2 of the 3 HI patients. The Spearman’s correlation coefficient between the clinical ichthyosis score and DLQI was 0.611 (P \u003c 0.05). Conclusion: We confirmed that Netherton syndrome and KID syndrome patients have a higher risk of allergy to food or environmental allergens and of skin infections, respectively. QOL impairment correlates with disease severity in HI and ISFs patients.", "subitem_description_language": "en", "subitem_description_type": "Abstract"}]}, "item_10_description_5": {"attribute_name": "内容記述", "attribute_value_mlt": [{"subitem_description": "ファイル公開:2019-11-01", "subitem_description_language": "ja", "subitem_description_type": "Other"}]}, "item_10_publisher_32": {"attribute_name": "出版者", "attribute_value_mlt": [{"subitem_publisher": "Elsevier", "subitem_publisher_language": "en"}]}, "item_10_rights_12": {"attribute_name": "権利", "attribute_value_mlt": [{"subitem_rights": "© 2018. This manuscript version is made available under the CC-BY-NC-ND 4.0 license http://creativecommons.org/licenses/by-nc-nd/4.0/", "subitem_rights_language": "en"}]}, "item_10_select_15": {"attribute_name": "著者版フラグ", "attribute_value_mlt": [{"subitem_select_item": "author"}]}, "item_10_source_id_61": {"attribute_name": "ISSN(print)", "attribute_value_mlt": [{"subitem_source_identifier": "0923-1811", "subitem_source_identifier_type": "PISSN"}]}, "item_1615787544753": {"attribute_name": "出版タイプ", "attribute_value_mlt": [{"subitem_version_resource": "http://purl.org/coar/version/c_ab4af688f83e57aa", "subitem_version_type": "AM"}]}, "item_access_right": {"attribute_name": "アクセス権", "attribute_value_mlt": [{"subitem_access_right": "open access", "subitem_access_right_uri": "http://purl.org/coar/access_right/c_abf2"}]}, "item_creator": {"attribute_name": "著者", "attribute_type": "creator", "attribute_value_mlt": [{"creatorNames": [{"creatorName": "Murase, Chiaki", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91029", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Takeichi, Takuya", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91030", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Shibata, Akitaka", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91031", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Nakatochi, Masahiro", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91032", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Kinoshita, Fumie", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91033", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Kubo, Akiharu", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91034", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Nakajima, Kimiko", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91035", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Ishii, Norito", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91036", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Amano, Hiroo", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91037", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Masuda, Koji", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91038", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Kawakami, Hiroshi", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91039", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Kanekura, Takuro", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91040", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Washio, Ken", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91041", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Asano, Masayuki", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91042", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Teramura, Kazuya", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91043", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Akasaka, Eijiro", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91044", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Tohyama, Mikiko", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91045", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Hatano, Yutaka", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91046", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Ochiai, Toyoko", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91047", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Moriwaki, Shinichi", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91048", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Sato, Tomotaka", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91049", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Ishida-Yamamoto, Akemi", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91050", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Seishima, Mariko", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91051", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Kurosawa, Michiko", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91052", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Ikeda, Shigaku", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91053", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "Akiyama, Masashi", "creatorNameLang": "en"}], "nameIdentifiers": [{"nameIdentifier": "91054", "nameIdentifierScheme": "WEKO"}]}]}, "item_files": {"attribute_name": "ファイル情報", "attribute_type": "file", "attribute_value_mlt": [{"accessrole": "open_date", "date": [{"dateType": "Available", "dateValue": "2019-11-01"}], "displaytype": "detail", "download_preview_message": "", "file_order": 0, "filename": "Revise.pdf", "filesize": [{"value": "627.7 kB"}], "format": "application/pdf", "future_date_message": "", "is_thumbnail": false, "licensetype": "license_note", "mimetype": "application/pdf", "size": 627700.0, "url": {"label": "Revise", "objectType": "fulltext", "url": "https://nagoya.repo.nii.ac.jp/record/27957/files/Revise.pdf"}, "version_id": "12dedf26-d8ed-4684-9c49-140c3e31715b"}]}, "item_keyword": {"attribute_name": "キーワード", "attribute_value_mlt": [{"subitem_subject": "Clinical ichthyosis score", "subitem_subject_scheme": "Other"}, {"subitem_subject": "Harlequin ichthyosis", "subitem_subject_scheme": "Other"}, {"subitem_subject": "Congenital ichthyosis", "subitem_subject_scheme": "Other"}, {"subitem_subject": "Syndromic form ichthyosis", "subitem_subject_scheme": "Other"}, {"subitem_subject": "Quality of life", "subitem_subject_scheme": "Other"}]}, "item_language": {"attribute_name": "言語", "attribute_value_mlt": [{"subitem_language": "eng"}]}, "item_resource_type": {"attribute_name": "資源タイプ", "attribute_value_mlt": [{"resourcetype": "journal article", "resourceuri": "http://purl.org/coar/resource_type/c_6501"}]}, "item_title": "Cross-sectional survey on disease severity in Japanese patients with harlequin ichthyosis/ichthyosis: Syndromic forms and quality-of-life analysis in a subgroup", "item_titles": {"attribute_name": "タイトル", "attribute_value_mlt": [{"subitem_title": "Cross-sectional survey on disease severity in Japanese patients with harlequin ichthyosis/ichthyosis: Syndromic forms and quality-of-life analysis in a subgroup", "subitem_title_language": "en"}]}, "item_type_id": "10", "owner": "1", "path": ["501"], "permalink_uri": "http://hdl.handle.net/2237/00030155", "pubdate": {"attribute_name": "PubDate", "attribute_value": "2019-05-10"}, "publish_date": "2019-05-10", "publish_status": "0", "recid": "27957", "relation": {}, "relation_version_is_last": true, "title": ["Cross-sectional survey on disease severity in Japanese patients with harlequin ichthyosis/ichthyosis: Syndromic forms and quality-of-life analysis in a subgroup"], "weko_shared_id": -1}
Cross-sectional survey on disease severity in Japanese patients with harlequin ichthyosis/ichthyosis: Syndromic forms and quality-of-life analysis in a subgroup
http://hdl.handle.net/2237/00030155
http://hdl.handle.net/2237/00030155b1a3b896-bc13-4f7a-8f85-b0f8b685aa4a
名前 / ファイル | ライセンス | アクション |
---|---|---|
Revise (627.7 kB)
|
|
Item type | 学術雑誌論文 / Journal Article(1) | |||||
---|---|---|---|---|---|---|
公開日 | 2019-05-10 | |||||
タイトル | ||||||
タイトル | Cross-sectional survey on disease severity in Japanese patients with harlequin ichthyosis/ichthyosis: Syndromic forms and quality-of-life analysis in a subgroup | |||||
言語 | en | |||||
著者 |
Murase, Chiaki
× Murase, Chiaki× Takeichi, Takuya× Shibata, Akitaka× Nakatochi, Masahiro× Kinoshita, Fumie× Kubo, Akiharu× Nakajima, Kimiko× Ishii, Norito× Amano, Hiroo× Masuda, Koji× Kawakami, Hiroshi× Kanekura, Takuro× Washio, Ken× Asano, Masayuki× Teramura, Kazuya× Akasaka, Eijiro× Tohyama, Mikiko× Hatano, Yutaka× Ochiai, Toyoko× Moriwaki, Shinichi× Sato, Tomotaka× Ishida-Yamamoto, Akemi× Seishima, Mariko× Kurosawa, Michiko× Ikeda, Shigaku× Akiyama, Masashi |
|||||
アクセス権 | ||||||
アクセス権 | open access | |||||
アクセス権URI | http://purl.org/coar/access_right/c_abf2 | |||||
権利 | ||||||
言語 | en | |||||
権利情報 | © 2018. This manuscript version is made available under the CC-BY-NC-ND 4.0 license http://creativecommons.org/licenses/by-nc-nd/4.0/ | |||||
キーワード | ||||||
主題Scheme | Other | |||||
主題 | Clinical ichthyosis score | |||||
キーワード | ||||||
主題Scheme | Other | |||||
主題 | Harlequin ichthyosis | |||||
キーワード | ||||||
主題Scheme | Other | |||||
主題 | Congenital ichthyosis | |||||
キーワード | ||||||
主題Scheme | Other | |||||
主題 | Syndromic form ichthyosis | |||||
キーワード | ||||||
主題Scheme | Other | |||||
主題 | Quality of life | |||||
抄録 | ||||||
内容記述 | Background: Congenital ichthyoses (CIs) adversely affect quality of life (QOL) in patients. However, the effects of CIs on patient QOL have not been studied sufficiently. Objective: To investigate the association between disease severity and QOL in patients with harlequin ichthyosis (HI) and ichthyosis: syndromic forms (ISFs) Methods: Clinical information of patients with HI and ISFs from 2010 to 2015 were obtained from 100 dermatology departments/divisions of principal institutes/hospitals throughout Japan. We examined the relationship between disease severity and QOL in patients with HI and ISFs. Patients who were aged 8 years or older and participated in a multicenter retrospective questionnaire survey in Japan were assessed by dermatology life quality index (DLQI, range of 0–30) and clinical ichthyosis score (range of 0–100). Results: Netherton syndrome patients had a significantly higher risk of allergy to food or environmental allergens than patients with other phenotypes. Keratitis-ichthyosis-deafness (KID) syndrome patients showed a significantly higher risk of skin infections than patients with other phenotypes. Complete data on DLQI were obtained from 13 patients, whose median age was 21 (8–71) years. Nine patients were male, and 4 were female. Systemic retinoids were administrated to 2 of the 3 HI patients. The Spearman’s correlation coefficient between the clinical ichthyosis score and DLQI was 0.611 (P < 0.05). Conclusion: We confirmed that Netherton syndrome and KID syndrome patients have a higher risk of allergy to food or environmental allergens and of skin infections, respectively. QOL impairment correlates with disease severity in HI and ISFs patients. | |||||
言語 | en | |||||
内容記述タイプ | Abstract | |||||
内容記述 | ||||||
内容記述 | ファイル公開:2019-11-01 | |||||
言語 | ja | |||||
内容記述タイプ | Other | |||||
出版者 | ||||||
言語 | en | |||||
出版者 | Elsevier | |||||
言語 | ||||||
言語 | eng | |||||
資源タイプ | ||||||
資源タイプresource | http://purl.org/coar/resource_type/c_6501 | |||||
タイプ | journal article | |||||
出版タイプ | ||||||
出版タイプ | AM | |||||
出版タイプResource | http://purl.org/coar/version/c_ab4af688f83e57aa | |||||
ISSN(print) | ||||||
収録物識別子タイプ | PISSN | |||||
収録物識別子 | 0923-1811 | |||||
書誌情報 |
en : Journal of Dermatological Science 巻 92, 号 2, p. 127-133, 発行日 2018-11 |
|||||
著者版フラグ | ||||||
値 | author |