| Item type |
itemtype_ver1(1) |
| 公開日 |
2022-01-13 |
| タイトル |
|
|
タイトル |
Cochlear implantation in patient with Charcot-Marie-Tooth disease |
|
言語 |
en |
| 著者 |
Kobayashi, Masumi
Yoshida, Tadao
Sugimoto, Satofumi
Teranishi, Masaaki
Hara, Daisuke
Kimata, Yukari
Sone, Michihiko
|
| アクセス権 |
|
|
アクセス権 |
open access |
|
アクセス権URI |
http://purl.org/coar/access_right/c_abf2 |
| 権利 |
|
|
言語 |
en |
|
権利情報 |
© 2021. This manuscript version is made available under the CC-BY-NC-ND 4.0 license http://creativecommons.org/licenses/by-nc-nd/4.0/ |
| キーワード |
|
|
主題Scheme |
Other |
|
主題 |
Charcot-Marie-Tooth disease |
| キーワード |
|
|
主題Scheme |
Other |
|
主題 |
Auditory neuropathy |
| キーワード |
|
|
主題Scheme |
Other |
|
主題 |
Cochlear implants |
| 内容記述 |
|
|
内容記述タイプ |
Abstract |
|
内容記述 |
Two patients with auditory neuropathy spectrum disorder (ANSD) considered to be associated with Charcot-Marie-Tooth (CMT) are reported. In case 1, a 23-year-old man presented with progressive bilateral sensorineural hearing loss (SNHL) from 10 years of age and was diagnosed with ANSD. He was later diagnosed with CMT by neurological testing. In case 2, a 16-year-old girl, the younger sister of the patient in case 1, presented with progressive SNHL with similar auditory findings since 6 years of age as those of her brother. Both cases underwent bilateral cochlear implantation. In case 1, the maximum discrimination score improved to 45% 24 months after the first side of cochlear implantation from 5% before the surgery. In case 2, the score was 5% 10 months after cochlear implant (CI) surgery from 0% before the surgery. CI treatment for CMT patients has been considered difficult because of both failure in synchronization of nerve conduction due to demyelination and axonal failure of the auditory nerve. Though slower progress compared to the average subset of patients receiving CI was seen, significant improvement was gradually observed in the present patients after bilateral cochlear implantations. CI is thus a viable option for rehabilitation of SNHL in CMT patients. |
|
言語 |
en |
| 出版者 |
|
|
出版者 |
Elsevier |
|
言語 |
en |
| 言語 |
|
|
言語 |
eng |
| 資源タイプ |
|
|
資源タイプ識別子 |
http://purl.org/coar/resource_type/c_6501 |
|
資源タイプ |
journal article |
| 出版タイプ |
|
|
出版タイプ |
AM |
|
出版タイプResource |
http://purl.org/coar/version/c_ab4af688f83e57aa |
| 関連情報 |
|
|
関連タイプ |
isVersionOf |
|
|
識別子タイプ |
DOI |
|
|
関連識別子 |
https://doi.org/10.1016/j.anl.2020.03.003 |
| 収録物識別子 |
|
|
収録物識別子タイプ |
PISSN |
|
収録物識別子 |
0385-8146 |
| 書誌情報 |
en : Auris Nasus Larynx
巻 48,
号 2,
p. 327-330,
発行日 2021-04-05
|
| ファイル公開日 |
|
|
日付 |
2022-04-05 |
|
日付タイプ |
Available |
ANL-D-20-00071_R2.pdf (338 KB)
